Reticulohistiocitosis cutánea difusa

Resumen

Las reticulohistiocitosis son un grupo de enfermedades raras, de etiología y patogenia desconocidas, caracterizadas por la proliferación de histiocitos (células de tipo no Langerhans) en diferentes tejidos; uno de los más afectados es la piel.

Se describen tres formas clínicas: el reticulohistiocitoma cutáneo solitario, la reticulohistiocitosis multicéntrica y la reticulohistiocitosis cutánea difusa.

Respecto del último grupo, se describieron solo 15 casos hasta la actualidad.

Se presenta el caso de un hombre de 63 años con diagnóstico de reticulohistiocitosis cutánea difusa.

Palabras clave: histiocitosis de células no Langerhans, reticulohistiocitosis, reticulohistiocitosis cutánea difusa.

Dermatol. Argent. 2019, 25 (2): 69-71

Diffuse cutaneous histiocytosis

Abstract

Reticulohistiocytosis is a group of rare diseases of unknown etiology and pathogenesis, characterized by the proliferation of histiocytes of the non-Langerhans cells type in different tissues, the skin is one of the most affected. So far three clinical forms have been described: solitary cutaneous reticulohistiocytoma, multicentric reticulohistiocytosis, and diffuse cutaneous reticulohistiocytosis. Regarding the last subgroup, only fifteen cases have been reported to date.

We present the case of a 63-year-old man with a diagnosis of diffuse cutaneous reticulohistiocytosis.

Key words: non Langerhans cell histiocytosis, reticulohistiocytosis,

diffuse cutaneous reticulohistiocytosis.

Dermatol. Argent. 2019, 25 (2): 69-71